E83.82: Disorders of pyrophosphate metabolism

New code · FY2026

Not billable: this is a header. Use one of the more specific codes below.

• New code, effective October 1, 2025 (FY2026).

Code breakdown

Coding notes

Excludes1 (from E83)

• dietary mineral deficiency (E58-E61)
• parathyroid disorders (E20-E21)
• vitamin D deficiency (E55.-)

Codes under E83.82

• E83.820 Generalized arterial calcification of infancy with unspecified genetic causality
• E83.821 ENPP1 deficiency causing generalized arterial calcification of infancy
• E83.822 ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2
• E83.823 ABCC6 deficiency causing generalized arterial calcification of infancy
• E83.824 ABCC6 deficiency causing pseudoxanthoma elasticum
• E83.825 CD73 deficiency causing arterial calcification

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All FY2026 ICD-10-CM changes

ICD-10-CM codes and descriptions are from the CMS and NCHS code files. Coverage is from the CMS Medicare Coverage Database billing and coding articles.