Home / ICD-10-CM / Chapter 4: Endocrine, nutritional and metabolic diseases (E00-E89) / Metabolic disorders (E70-E88)

E83.822: ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2

ICD-10-CM code E83.822

New code ยท FY2026

Billable: use this code on claims.

  • New code, effective October 1, 2025 (FY2026).

Code breakdown

E83.822

  1. E83CategoryDisorders of mineral metabolism
  2. 8Character 4Other disorders of mineral metabolism
  3. 2Character 5Disorders of pyrophosphate metabolism
  4. 2Character 6ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2

Coding notes

Excludes1 (from E83)

  • dietary mineral deficiency (E58-E61)
  • parathyroid disorders (E20-E21)
  • vitamin D deficiency (E55.-)

Medicare coverage

E83.822 is listed as a covered diagnosis in 1 Medicare billing and coding article:

  • A57122 Billing and Coding: Parathormone (Parathyroid Hormone)

Check this code

All FY2026 ICD-10-CM changes

ICD-10-CM codes and descriptions are from the CMS and NCHS code files. Coverage is from the CMS Medicare Coverage Database billing and coding articles.