E78.01: Familial hypercholesterolemia

No longer billable · FY2026

Not billable: this is a header. Use one of the more specific codes below.

• No longer billable from October 1, 2025: it became a header for more specific codes: E78.010, E78.011, E78.019.

Code breakdown

Coding notes

Excludes1 (from E78)

• sphingolipidosis (E75.0-E75.3)

Codes under E78.01

• E78.010 Homozygous familial hypercholesterolemia [HoFH]
• E78.011 Heterozygous familial hypercholesterolemia [HeFH]
• E78.019 Familial hypercholesterolemia, unspecified

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All FY2026 ICD-10-CM changes

ICD-10-CM codes and descriptions are from the CMS and NCHS code files. Coverage is from the CMS Medicare Coverage Database billing and coding articles.