Home / ICD-10-CM / Genetic disorders, not elsewhere classified (QA0-QA1)

QA1.71: Lynch syndrome

ICD-10-CM code QA1.71

New code ยท FY2027

Billable: use this code on claims.

  • New code, effective October 1, 2026 (FY2027).

Code breakdown

QA1.71

  1. QA1CategoryGenetic disorders associated with neoplasms, not elsewhere classified
  2. 7Character 4Inherited neoplasm predisposition syndromes involving multiple systems, not elsewhere classified
  3. 1Character 5Lynch syndrome

Coding notes

Inclusion terms

  • Hereditary nonpolyposis colorectal cancer susceptibility
  • Lynch syndrome due to EPCAM
  • Lynch syndrome due to MLH1
  • Lynch syndrome due to MSH2
  • Lynch syndrome due to MSH6
  • Lynch syndrome due to PMS2

Excludes2 (from QA1)

  • multiple endocrine neoplasia [MEN] syndromes (E31.2-)

Code also (from QA1)

  • , if applicable, any associated conditions, such as:
  • genetic susceptibility to malignant neoplasm by site (Z15.0-)
  • malignant neoplasms (C00.0-C96.9)
  • personal history of malignant neoplasm (Z85.-)

Check this code

All FY2027 ICD-10-CM changes

ICD-10-CM codes and descriptions are from the CMS and NCHS code files. Coverage is from the CMS Medicare Coverage Database billing and coding articles.