Q87.A: Loeys-Dietz syndrome

New code · FY2027

Billable: use this code on claims.

• New code, effective October 1, 2026 (FY2027). Before that, this condition was coded as Q87.89.

Code breakdown

Coding notes

Excludes1

• arterial tortuosity syndrome (Q87.82)
• Ehlers-Danlos syndrome (Q79.6)
• Marfan syndrome (Q87.40-Q87.43)
• other systemic involvement of connective tissue (M35)

Use additional code (from Q87)

• code(s) to identify all associated manifestations

Medicare coverage

Q87.A is listed as a covered diagnosis in 4 Medicare billing and coding articles:

• A59847 Billing and Coding: MolDX: Genetic Testing in Heritable Thoracic Aortic Disease
• A59860 Billing and Coding: MolDX: Genetic Testing in Heritable Thoracic Aortic Disease
• A59868 Billing and Coding: MolDX: Genetic Testing in Heritable Thoracic Aortic Disease
• A59908 Billing and Coding: MolDX: Genetic Testing in Heritable Thoracic Aortic Disease

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All FY2027 ICD-10-CM changes

ICD-10-CM codes and descriptions are from the CMS and NCHS code files. Coverage is from the CMS Medicare Coverage Database billing and coding articles.