Home / ICD-10-CM / Chapter 14: Diseases of the genitourinary system (N00-N99) / Glomerular diseases (N00-N08)

N04.B1: Nephrotic syndrome with idiopathic immune complex membranoproliferative glomerulonephritis (IC-MPGN)

ICD-10-CM code N04.B1

New code · FY2026

Billable: use this code on claims.

  • New code, effective October 1, 2025 (FY2026).

Code breakdown

N04.B1

  1. N04CategoryNephrotic syndrome
  2. BCharacter 4Nephrotic syndrome with immune complex membranoproliferative glomerulonephritis (IC-MPGN)
  3. 1Character 5Nephrotic syndrome with idiopathic immune complex membranoproliferative glomerulonephritis (IC-MPGN)

Coding notes

Includes (from N04)

  • congenital nephrotic syndrome
  • lipoid nephrosis

Medicare coverage

N04.B1 is listed as a covered diagnosis in 2 Medicare billing and coding articles:

  • A54548 Billing and Coding: Eculizumab, and Biosimilars: EPYSQLI®-eculizumab-aagh, and BKEMV™-eculizumab-aeeb
  • A59186 Billing and Coding: Magnesium

Check this code

All FY2026 ICD-10-CM changes

ICD-10-CM codes and descriptions are from the CMS and NCHS code files. Coverage is from the CMS Medicare Coverage Database billing and coding articles.