I42.81: Arrhythmogenic cardiomyopathy

New code · FY2027

Billable: use this code on claims.

• New code, effective October 1, 2026 (FY2027). Before that, this condition was coded as I42.8.

Code breakdown

Coding notes

Includes (from I42)

• myocardiopathy

Excludes2 (from I42)

• ischemic cardiomyopathy (I25.5)
• peripartum cardiomyopathy (O90.3)
• ventricular hypertrophy (I51.7)

Code first (from I42)

• pre-existing cardiomyopathy complicating pregnancy and puerperium (O99.4)

Medicare coverage

I42.81 is listed as a covered diagnosis in 32 Medicare billing and coding articles:

• A52850 Billing and Coding: Cardiac Catheterization and Coronary Angiography
• A52868 Billing and Coding: Transesophageal Echocardiography (TEE)
• A56391 Billing and Coding: Implantable Automatic Defibrillators
• A56476 Billing and Coding: Cardiac Radionuclide Imaging
• A56500 Billing and Coding: Cardiac Catheterization and Coronary Angiography
• A56505 Billing and Coding: Transesophageal Echocardiography (TEE)
• A56580 Billing and Coding: Computerized Axial Tomography (CT), Thorax
• A56605 Billing and Coding: B-type Natriuretic Peptide (BNP) Testing
• A56625 Billing and Coding: Echocardiography
• A56691 Billing and Coding: Cardiac Computed Tomography & Angiography (CCTA)

…and 22 more. Check the coverage tool for your CPT code.

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All FY2027 ICD-10-CM changes

ICD-10-CM codes and descriptions are from the CMS and NCHS code files. Coverage is from the CMS Medicare Coverage Database billing and coding articles.