I27.841: Fontan-associated lymphatic dysfunction

New code · FY2026

Billable: use this code on claims.

• New code, effective October 1, 2025 (FY2026).

Code breakdown

Coding notes

Code also

• associated conditions such as:
• chylothorax (J94.0)
• Fontan associated protein-losing enteropathy (K90.49)
• plastic (obstructive) bronchitis (J44.89)

Medicare coverage

I27.841 is listed as a covered diagnosis in 14 Medicare billing and coding articles:

• A56476 Billing and Coding: Cardiac Radionuclide Imaging
• A56500 Billing and Coding: Cardiac Catheterization and Coronary Angiography
• A56580 Billing and Coding: Computerized Axial Tomography (CT), Thorax
• A56625 Billing and Coding: Echocardiography
• A56691 Billing and Coding: Cardiac Computed Tomography & Angiography (CCTA)
• A56717 Billing and Coding: Respiratory Therapy (Respiratory Care)
• A56730 Billing and Coding: Respiratory Therapy and Oximetry Services
• A56775 Billing and Coding: Magnetic Resonance Angiography
• A56852 Billing and Coding: Laparoscopic Sleeve Gastrectomy for Severe Obesity
• A57224 Billing and Coding: Respiratory Care

…and 4 more. Check the coverage tool for your CPT code.

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All FY2026 ICD-10-CM changes

ICD-10-CM codes and descriptions are from the CMS and NCHS code files. Coverage is from the CMS Medicare Coverage Database billing and coding articles.